Letter to the Editor

Familial Autosomal Dominant Sensorineural Hearing Loss Associated with Dilated Cardiomyopathy

Authors: Manu Kaushik, MD, Venkata M. Alla, MD, Ritu Madan, MD, Yeruva M. Reddy, MD, Chandra K. Nair, MD, Prateek K. Gupta, MBBS

Abstract

To the Editor:


Familial forms comprise about a third of all idiopathic cardiomyopathies and are often associated with non-cardiac manifestation. Awareness of these manifestations is important for internists to successfully diagnose these conditions. A rare form of familial dilated cardiomyopathy associated with autosomal dominant sensorineural hearing loss has been described. To the best of our knowledge, only two families with this pattern of familial cardiomyopathies have been previously reported in the literature. We report a case of cardiomyopathy that conforms to this rarely reported familial form.

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