Case Report

Central Retinal Vein Occlusion in Sickle Cell Disease

Authors: Syed Hasan, MD, Mamoon Elbedawi, MD, Oswaldo Castro, MD, Mark Gladwin, MD, Alan Palestine, MD

Abstract

Central retinal vein occlusion has not been reported previously in patients with sickle cell anemia. We describe the case of a 31-year-old man with sickle cell anemia who developed this complication. The search for risk factors for central retinal vein occlusion in this young patient revealed protein S deficiency and a history of iron deficiency. He was treated with anticoagulation therapy, and his vision improved gradually.

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