Case Report

Multiorgan Failure Caused by Intravascular Lymphoma: A Highly Rare and Malignant Hemopathy Mimicking Multisystemic Disease

Authors: T Weitten, MD, S Rozan-Rodier, MD, P Guiot, MD, E Andrès, MD, Y Mootien, MD

Abstract

This manuscript describing a case of intravascular lmphoma, displays the difficulties underlying its diagnosis. We emphasize that intravascular lymphoma should be considered in patients with multisystemic manifestations without obvious etiology. Despite the heterogeneous presentation of this lymphoma, some clinical and biological investigations should prevail clinicians to do tissue biopsy which is required to make the diagnosis.


Key Points


* Intravascular lymphoma is a rare, disseminated and aggressive non-Hodgkin lymphoma.


* Clinical aspects of intravascular lymphoma are extremely heterogeneous.


* Intravascular lymphoma should be considered in patients with multisystemic manifestations without obvious etiology, particularly if accompanied by telangiectasias.


* Biopsy of an involved organ is required to make the diagnosis.

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