Letter to the Editor

Massive Cystic Liver in a Patient with Autosomal Dominant Polycystic Kidney Disease

Authors: Tanmay S. Panchabhai, MD, George R. Aronoff, MD, MS

Abstract

To the Editor:


We present the case of a 55-year-old woman with end-stage kidney disease requiring hemodialysis. She was found to have autosomal dominant polycystic kidney disease (ADPCKD) in 1999. Her mother was diagnosed with ADPCKD in the same year and had a deceased donor kidney transplant. The patient underwent a right nephrectomy in 2006 to facilitate kidney transplantation. The left kidney was not removed at that time because of dense adhesions and a massively enlarged liver. Because the enlarging liver continued to fill the abdominal cavity, an elective left nephrectomy was done during the present hospitalization. The patient is currently awaiting a deceased donor kidney transplant. Detailed questioning revealed that the patient used oral contraceptive pills for 10 years. We present the computed tomography (CT) scan images depicting a massively enlarged cystic liver and a moderately enlarged left kidney before nephrectomy (Figs. 1, 2).

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