Case Report

Mounier-Kuhn Syndrome: Report of 8 Cases of Tracheobronchomegaly With Associated Complications

Mounier-Kuhn syndrome is a rare congenital abnormality characterized by atrophy or absence of elastic fibers and thinning of smooth muscle layer in the trachea and main bronchi. These airways are thus flaccid and markedly dilated on inspiration and collapsed on expiration. First- to fourth-order bronchi are affected. There is an…

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